Shock cardiogénico causado por implantación anómala de arteria coronaria

F. Alejandro Donoso, R. Pablo Cruces, R. Franco Díaz, C. Cristián Clavería

Resultado de la investigación: Contribución a una revistaArtículorevisión exhaustiva

Resumen

Background: Congenital anomalies of coronary implantation are unfrequent, only 1% of congenital cardiopathies. The anomalous origin of left coronary artery from the pulmonary artery (alcapa) is far more frequent and its manifestations usually arise from myocardial ischemia. Case-report: A male infant 2 month-old that was admitted at our unit with cardiogenic shock and severe metabolic acidosis. The chest X-ray showed cardiomegaly and the echocardiography found diastolic left ventricular dysfunction, with left ventricular shortening fraction of 13%, evidence of dilated cardiomyopathy and anomalous insertion of left coronary artery in the left postero-lateral side of pulmonary artery trunk. Connected to mechanical ventilation, he received crystalloids, hemoderivatives, inotropic hemodynamic support, furosemide and calcium continuous infusion. Moderate hypothermia appeared the second and third day after admission. He developed multiorgan dysfunction with cardiogenic shock and non-oliguric renal failure. At the fifth day, he was stable enough to try surgical repair. Coronary transference from pulmonary artery trunk to aorta was performed without serious adverse events. Finally, a month after his admission, he was discharged home. An ambulatory evaluation 3 months after showed normal cardiac function. Comment: Myocardial ischemia is the main manifestation of alcapa. Its signs and symptoms usually start at the end of the first gestational trimester, according to the lower pulmonary vascular resistance. The clinician must be aware in every patient with cardiogenic shock and dilated cardiomyopathy. Surgical repair must be done, although good outcomes can be achieved only with early and reliable diagnosis.

Título traducido de la contribuciónCardiogenic shock caused by coronary artery anomalous implantation
Idioma originalEspañol
Páginas (desde-hasta)509-515
Número de páginas7
PublicaciónRevista Chilena de Pediatria
Volumen79
N.º5
EstadoPublicada - oct 2008

Palabras clave

  • Anomalous coronary artery
  • Cardiogenic shock
  • Congenital heart disease

Áreas temáticas de ASJC Scopus

  • Pediatría, perinaltología y salud infantil

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